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A Challenging Case of Kikuchi-Fujimoto Disease Associated with Systemic Lupus Erythematosus and Review of the Literature #MMPMID29785310
G?man M; Vl?d?reanu AM; Dobrea C; Onisâi M; Marinescu C; Voican I; Vasile D; Bumbea H; Cî?leanu D
Case Rep Hematol 2018[]; 2018 (ä): ä PMID29785310show ga
Kikuchi?Fujimoto disease (KFD) or histiocytic necrotizing lymphadenitis is a rare disease that is frequently underdiagnosed due to clinical features that are similar to those of non-Hodgkin lymphomas, systemic lupus erythematosus (SLE), or infectious reactive lymphadenopathy. An excisional biopsy is required. We report a young Caucasian female diagnosed with KFD with skin lesions, complicating with SLE. The clinical course, laboratory, and CT findings are described, as are histopathologic features, for a better recognition of this rare disorder in clinical practice.